Clinical History
Diagnosis: Dyke-Davidoff-Masson syndrome
Comment :
Figure1 : right cerebral atrophy with prominent CSF space .
Figure2: thickening of skull vault and overdevelopment of frontal
sinuses on right side .
Cerebral hemiatrophy or Dyke-Davidoff-Masson syndrome is a condition
characterized by seizures, facial asymmetry, contralateral hemiplegia
or hemiparesis, and mental retardation. These findings are due to
cerebral injury that may occur early in life or in utero. The radiological
features are unilateral loss of cerebral volume and associated compensatory
bone alterations in the calvarium, like thickening, hyperpneumatization
of the paranasal sinuses and mastoid cells and elevation of the
petrous ridge.
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