Clinical History
A 55-year-old lady presented with stroke.
Diagnosis:
Pulmonary Arteriovenous Malformation
Comment :
CT scan of thorax and pulmonary angiogram revealed multiple
pulmonary arteriovenous malformations. Hepatic angiogram showed
that the hepatic arteries were hypertrophied with increased tortuosity.
Fast AV transit was noted diffusely in the whole liver. Features
were suggestive of numerous AV shunts at microscopic level in liver
parenchyma. A lobular aneurysm was noted in bifurcation of splenic
artery. The diagnosis is Hereditary Hemorrhagic Telangiectasia.
(HHT or Osler-Weber-Rendu syndrome).
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